Familial Tuberous Sclerosis Complex:

Tuberous Sclerosis Complex an a Patient Presenting in Status Epilepticus


  • Dr. Obiabo Yahaya Olugbo


tuberous sclerosis complex, status epilepticus, epilepsy


Tuberous sclerosis complex is a rare multi-systemic disorder that could be complicated by disabling neurological manifestations including intractable epilepsy. It is an autosomal dominant disorder with variable penetrance. Familial tuberous sclerosis probably occurs more often than is reported in the literature. This article reports on a Nigerian man with tuberous sclerosis complex who presented in status epilepticus with documentation of tuberous sclerosis in his family and discussed the manifestations, diagnostic criteria, clinical evaluation, investigation and management of patients with tuberous sclerosis complex.

Author Biography

Dr. Obiabo Yahaya Olugbo

Neurology Unit, Department of Medicine, Delta State University Teaching
Hospital, Oghara.

Tel: +234(0)8035785839


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How to Cite

Olugbo OY. Familial Tuberous Sclerosis Complex: : Tuberous Sclerosis Complex an a Patient Presenting in Status Epilepticus. AJTMBR [Internet]. 2012 Sep. 1 [cited 2023 Mar. 24];1(4):95-103. Available from: https://ajtmbr.org.ng/index.php/home/article/view/33